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fisiopatologia sodeman pdf extra quality
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7. ABORDAGENS TERAPÊUTICAS

7.1. Estratégias Antioxidantes

| Agente | Mecanismo | Evidência de eficácia | |--------|-----------|------------------------| | Etil‑ester de ácido α‑lipoico (ALA‑EE) | Regenera glutationa (GSH) | Estudos em mouse SOD1‑G93A → aumento de sobrevida em 15 % | | N‑acetilcisteína (NAC) | Precursor de GSH | Redução de γ‑H2AX foci em fibroblastos de pacientes | | Mimeticos de SOD (MnTBAP, Tempol) | Atuam como SOD farmacológica | Melhora de parâmetros respiratórios em modelos de SOD2‑deficiência | I can offer a valuable

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